Missing content? – Request curation!
Request curation for specific Genes, Variants, or PubMed publications.
Have questions, comments, or suggestions? - Let us know!
Email us at : ckbsupport@jax.org
Gene | PBRM1 |
Variant | S681R |
Impact List | missense |
Protein Effect | unknown |
Gene Variant Descriptions | PBRM1 S681R lies within Bromo domain 5 of the Pbrm1 protein (UniProt.org). S681R has been identified in the scientific literature (PMID: 29301960), but has not been biochemically characterized and therefore, its effect on Pbrm1 protein function is unknown (PubMed, Dec 2022). |
Associated Drug Resistance | |
Category Variants Paths |
PBRM1 mutant PBRM1 S681R |
Transcript | NM_018313.4 |
gDNA | chr3:g.52609837A>C |
cDNA | c.2043T>G |
Protein | p.S681R |
Source Database | RefSeq |
Genome Build | GRCh38/hg38 |
Transcript | gDNA | cDNA | Protein | Source Database | Genome Build |
---|---|---|---|---|---|
XM_017006725 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006761 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006727 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_011533902.3 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
NM_181042.4 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006762 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006754 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
NM_001350077.1 | chr3:g.52609937_52609938delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_011533903.3 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006753 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006748 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006753.2 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006758.1 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006726.1 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006743 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006752 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006754.1 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006763 | chr3:g.52609937_52609938delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006728 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006728.1 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006752.1 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_011533903 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006750 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006729 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_011533900.3 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006726 | chr3:g.52615368_52615369delGAinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
NM_001350075.1 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006749.1 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006732 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006748.1 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_011533900 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
NM_018313 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
NM_001350078.1 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006757 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006765 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006725.1 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006749 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006743.2 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006727.1 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
NM_001350076.1 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006729.2 | chr3:g.52615368_52615369delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_024453618.1 | chr3:g.52609937_52609938delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
NM_018313.4 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006760 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
NM_001350074.1 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_024453619.1 | chr3:g.52609937_52609938delTCinsCG | c.2041_2042delTCinsCG | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006732.1 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006758 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_017006750.1 | chr3:g.52609837A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
XM_011533902 | chr3:g.52609945A>C | c.2043T>G | p.S681R | RefSeq | GRCh38/hg38 |
Molecular Profile | Indication/Tumor Type | Response Type | Therapy Name | Approval Status | Evidence Type | Efficacy Evidence | References |
---|---|---|---|---|---|---|---|
PBRM1 S681R | clear cell renal cell carcinoma | predicted - sensitive | Nivolumab | Case Reports/Case Series | Actionable | In a clinical study, Opdivo (nivolumab) treatment resulted in partial response in a patient with renal clear cell carcinoma harboring PBRM1 S681R (PMID: 29301960). | 29301960 |